The Hirayama Disease’s MRI Features and Literature Review_West China Medical Journal

Authors：

YI Xuebing ¹ , DENG Kaihong ² , ZHANG Dezhou ¹

1.Department of Radiology，Sichuan Province Orthopedics Hospital;2.Department of Radiology，West China Hospital，Sichuan University，Chengdu 610041，China;

Corresponding author：

Keywords：

平山病; 磁共振成像

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目的:通过分析平山病的磁共振成像(MRI)表现特点和结合文献复习，提高其诊断水平。方法:报道1例经临床证实的平山病患者的MRI表现，并复习文献，探讨MRI表现的相关发病机制及病理解剖基础。结果:采用西门子Sonata 1.5T磁共振机，先取生理状态下颈椎MRI检查，显示脊髓前角非对称性萎缩和脊髓背侧硬膜外静脉丛扩张；再行屈颈状态下MRI检查，可见颈髓的硬脊膜后壁向前推移，下段颈髓局限受压变细征。结论:平山病有特征性MRI表现，结合临床、常规位和功能位屈颈状态的MRI检查，可以提示平山病。

Citation： YI Xuebing,DENG Kaihong,ZHANG Dezhou. The Hirayama Disease’s MRI Features and Literature Review. West China Medical Journal, 2009, 24(1): 150-152. doi: Copy

1.	Robberecht W，Aguirre T，Van den Bosch L，et al.Familial juvenile focal amyotrophy of the upper extremity (Hirayama Disease).Superoxide dismutase 1 genotype and activity[J].Arch Neurol，1997，54(1):46-50..
2.	Schroder R，Keller E，Flacke S，et al.MRI findings in Hirayama’s disease:flexioninduced cervical myelopathy or intrinsic motor neuron disease?[J]J Neurol，1999，246(11):10691074..
3.	Hirayama K，Tokumamu Y.Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity[J].Neurology，2000，54(10):1922-1926..
4.	Chen CJ，Chen CM，Wu CL，et al.Hirayama Disease:MR Diagnosis[J].AJN R Am J Neuroradiol，1998，19(2):365-384..
5.	Bland JH.Basic anatomy[M].2nd ed.Philadelphia，Pa:Saunders，1994:41-70..
6.	Toma S，Shiozawa Z.Amyotrophic cervical myelopathy in adolescence[J].J Neurol Neurosurg Psychiatry，1995，58 (1):56-64.

1. Robberecht W，Aguirre T，Van den Bosch L，et al.Familial juvenile focal amyotrophy of the upper extremity (Hirayama Disease).Superoxide dismutase 1 genotype and activity[J].Arch Neurol，1997，54(1):46-50..
2. Schroder R，Keller E，Flacke S，et al.MRI findings in Hirayama’s disease:flexioninduced cervical myelopathy or intrinsic motor neuron disease?[J]J Neurol，1999，246(11):10691074..
3. Hirayama K，Tokumamu Y.Cervical dural sac and spinal cord in juvenile muscular atrophy of distal upper extremity[J].Neurology，2000，54(10):1922-1926..
4. Chen CJ，Chen CM，Wu CL，et al.Hirayama Disease:MR Diagnosis[J].AJN R Am J Neuroradiol，1998，19(2):365-384..
5. Bland JH.Basic anatomy[M].2nd ed.Philadelphia，Pa:Saunders，1994:41-70..
6. Toma S，Shiozawa Z.Amyotrophic cervical myelopathy in adolescence[J].J Neurol Neurosurg Psychiatry，1995，58 (1):56-64.

West China Medical Journal

The Hirayama Disease’s MRI Features and Literature Review

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