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find Keyword "内脏转位" 3 results
  • Kartagener Syndrome: Three Cases Report and Literature Review

    Objective To improve the knowledge of kartagener syndrome and the understanding of primary ciliary dyskinesia ( PCD) . Methods Three cases of Kartagener syndrome were reported and analyzed on clinical manifestations, symptoms, imaging appearances of chest, and family history. Meanwhile the related literatures were reviewed. Results The three patients deserved special recognition because of recurrent upper and lower respiratory tract infection. Of them, the third case showed mainly the symptoms of nasosinusitis at an early age, and the distinct pulmonary symptoms appeared in his adulthood. Further examination showed that the triad of chronic sinusitis, bronchiectasis, and situs inversus is present in all cases. The parents of the two cases were consanguineous marriaged. Examination of the bronchial mucosal biopsy specimen of the first case under transmission electron microscopy showed cilia with the absence of inner dynein arms. The three cases got improvement after treatment of anti-infection and expectorant. Conclusion For patients with recurring infection in the upper and lower respiratory tract from infancy, the possibility of PCD should be considered no matter whether a situs inversus exists.

    Release date:2016-09-13 04:07 Export PDF Favorites Scan
  • Endoscopic reverse biliary tract stent placement via choledochus in treatment of situs inversus totalis complicated with choledocholithiasis

    ObjectiveTo summarize experience of endoscopic reverse biliary tract stent placement via choledochus in treatment of situs inversus totalis complicated with choledocholithiasis.MethodThe clinical data of one patient with situs inversus totalis complicated with choledocholithiasis in the Department of Tumor Surgery of Lanzhou University Second Hospital were retrospectively analyzed.ResultsThe ERCP was failed at the first admission, followed by the cholecystectomy plus choledocholithotomy plus T-tube drainage, the stones were removed. Two months later, choledochoscopy revealed multiple choledocholithiasis, then the holmium laser lithotripsy and bile duct stent placement was performed at the secondary admission, the postoperative recovery was good, it had been more than 2 months after the surgery, no stone recurrence occurred.ConclusionEndoscopic reverse biliary tract stent placement via choledochus is feasible, which can be used as an option for treatment of patient with situs inversus totalis complicated with choledocholithiasis.

    Release date:2019-03-18 05:29 Export PDF Favorites Scan
  • Kartagener 综合征四例报告并文献复习

    目的探讨 Kartagener 综合征的临床特点,提高该病的诊治水平。方法回顾本院呼吸内科收治的 4 例 Kartagener 综合征患者的临床资料,综合复习相关文献后进行分析。结果4 例 Kartagener 综合征中,男 3 例,女 1 例,年龄 24~51 岁。1 例父母为表兄妹近亲结婚。患者均因咳嗽、咳痰,伴或不伴咯血痰、胸闷、气促、喘息、浮肿、发热等症状就诊。1 例在外院确诊 Kartagener 综合征、肺源性心脏病,余 3 例 CT 影像等检查提示存在内脏转位、支气管扩张、鼻窦炎三联征,入院后确诊 Kartagener 综合征。4 例均给抗感染、祛痰、分泌物引流治疗,合并肺源性心脏病者予以无创呼吸机辅助通气、抗心力衰竭等治疗后,病情缓解出院。复习国内外文献,咳嗽、咳痰、咯血、气促是 Kartagener 综合征就诊的主要症状;预防感染、及时控制感染是治疗 Kartagener 综合征的关键。随着对 Kartagener 综合征的基因遗传学研究的深入,有望寻找到有效的办法以早期诊断,有效治疗,甚至减少发病。结论Kartagener 综合征是一种以内脏转位、支气管扩张、鼻窦炎为表现的罕见的先天遗传性疾病。提高临床医生对该病的认识,早期诊断,综合治疗,有效控制慢性气道炎症,是控制疾病进展、改善预后的有效方法。

    Release date:2019-07-19 02:21 Export PDF Favorites Scan
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