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find Keyword "海马硬化" 15 results
  • 海马硬化与癫痫

    难治性癫痫的患者常常伴有海马硬化, 是耐药性癫痫的主要致病因素。海马硬化在长期复杂的癫痫发作过程中逐渐形成, 两者之间的作用关系一直是癫痫领域的研究热点。现结合近年来国内外研究的新进展探讨海马硬化与癫痫之间的关系, 为颞叶癫痫的临床诊疗提供新的思路

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  • Risks of seizure recurrence from antiepileptic drug withdrawal among seizure-free patients for more than three years

    ObjectiveTo determine the outcome of antiepileptic drugs (AEDs) withdrawal in patients who had been seizure-free for more than two years. MethodsPatients with epilepsy who had been seizure-free for at least two years and decided to stop AEDs therapy gradually were checked on every two months for seizure relapse. The inclusion criteria were:①diagnosis of epilepsy, defined as at least two unprovoked seizures at least 24 hours apart; ②patients remained seizure-free for at least 24 consecutive months during AEDs therapy; ③patients expressed a desire to discontinue AEDs therapy gradually and agreed to return for regular follow-ups; and④electroencephalogram (EEG) showed no epileptic discharge. The time to a seizure relapse and predictive factors were analyzed by survival methods, including sex; age at seizure onset; number of episodes; seizure-free period before AEDs withdrawal; duration of follow-up after AEDs withdrawal; AEDs tapering off period (taper period); results from brain MRI; EEG before seizure-free; EEG before drug withdrawal; seizure type (classified as generalized, partial, or multiple types based on history); the number of AEDs administered for long-term seizure control. A log-rank test was used for univariate analysis, and a Cox proportional hazard model was used for multivariate analysis. ResultsSixty-eight patients (39 male, 29 female) were admithed. The relapsed rate was 23.5%. Univariate analysis and multivariate Cox regression analysis indicated that multiple AEDs, hippocampal sclerosis and withdrawal time were significantly correlated with seizure recurrence and those were significant independent predictive factors, with hazard ratio were 0.861, 2.223 and 2.137 respectively. ConclusionsThe relapsed rate in our study was similar to other studies. Distinguishing variables, such as multiple AEDs, hippocampal sclerosis and withdrawal time, need to be considered when decide to withdraw. Therefore, our recommendation is that after two years of being seizure-free, patients could consider withdrawal unless they are hippocampal sclerosis patients.

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  • A Study of Cytokine Changes in the Cerebrospinal Fluid of Mesial Temporal Lobe Epilepsy Patients with Hippocampal Sclerosis

    ObjectiveTo study the cytokine changes in the cerebrospinal fluid (CSF) of mesial temporal lobe epilepsy (MTLE) patients, and the mechanism of the development of hippocampal sclerosis. MethodsFifty MTLE patients who sought treatment from January 2013 to March 2014 were included in the study. Clinical features were investigated. All CSF samples of the 59 patients along with 19 samples of the control group were tested for 12 common cytokines using a chemokine magnetic bead panel. Data were statistically analyzed. ResultsClinical features showed no significant difference between hippocampal sclerosis and non-hippocampal sclerosis patients. Interleukin (IL)-1 receptor antagonist (RA), IL-4 and IL-9 expression decreased, and tumor necrosis factor (TNF)-α, IL-3 and IL-5 expression increased. Up-regulation of TNF-α was significantly different between hippocampal sclerosis and non-hippocampal sclerosis patients. ConclusionIL-1RA, IL-3, IL-4, IL-5 and IL-9 changes may be non-specific seizure-related cytokine regulation. TNF-α is associated with hippocampal sclerosis pathology. TNF-α is a possible pathological element in hippocampal sclerosis development.

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  • A study of autophagy flux abnormal block in atypical hippocampal sclerosis

    ObjectiveThe abnormal autophagy fluxis involved in the pathophysiological process of drug-resistance temporal lobe epilepsy (TLE).Hippocampal sclerosis (HS) is the main pathological type of drug-resistance TLE.Different subtypes of HS have various prognosis, etiology and pathophysiology.However, whether theabnormal block ofautophagy flux involved in this process has not been reported.This study proposed a preliminary comparison of autophagy fluxin typical and atypical HS to investigate the potential pathogenesis and drug-resistance mechanism of atypical HS. MethodsSurgical excision of hippocampal and temporal lobe epilepsy foci were performed in 17 patients with drug-resistance TLE.Patients were grouped according to the HS classification issued by International League Against Epilepsy in 2013.The distribution and expression of LC3B, beclin-1 and P62 were detected by immunohistochemistry and Western blot in each group. ResultsLC3B, beclin-1 and P62 are mainly expressed in neuronal cytoplasm, which is consistent with previous reports.Taking β-actin as internal reference, we found that LC3B and Beclin-1, the downstream products of autophagy flux, have increased significantly (P < 0.01) in the atypical HS group compared to typical HS group.However, the autophagy flux substrate P62 has no difference between the groups.This result suggested that compared with the typical HS group, atypical HS group had autophagy substrate accumulation and autophagy flux abnormal block.Besides, we found that glyceraldehycle-3-phosphate dehydrogenase(GAPDH) was significantly different between the two groups (P=0.003). ConclusionThere is abnormal phenomenon of autophagy flux in atypical HS, and GAPDH elevation may be involved in its mechanism, which might provide new targets and ideas for future treatment of atypical HS.

    Release date:2017-09-26 05:09 Export PDF Favorites Scan
  • 海马硬化相关的颞叶癫痫的短期和长期手术预后:与神经病理学的关系

    海马硬化(Hippocampal sclerosis, HS)是接受手术治疗的难治性颞叶癫痫(Temporal lobe epilepsy, TLE)患者中最常见的病理类型。国际抗癫痫联盟(ILAE)最近按细胞丢失的不同类型提出一个新的HS分类。研究旨在探讨HS不同类型之间的关系、病因、有HS的耐药性TLE患者术后短期及长期预后。213例术后病理诊断为HS的患者纳入此研究,每例至少随访2年时间。患者依照ILAE标准进行HS分类,并进一步分为单纯HS(Isolated HS, IHS)、HS伴皮质发育不良(Focal cortical dysplasia, FCD IIIa)和HS伴其他病灶。将患者临床及病理特点与其以标准来评价的术后预后进行对比。主要发现如下:① 1型HS癫痫病程较长;② 80%以上患者短期和长期预后均在EngelⅠ级,无论何种HS类型和相关病理学改变;③短期和长期的术后预后在完全无癫痫发作的患者(EngelⅠa级)中较不令人满意,2型HS患者长期预后较1型更好;④无论HS为何种类型,伴有FCD的患者预后较差;⑤较短的癫痫持续时间与EngelⅠa级预后有显著关联。研究结果表明HS类型与相关病理改变能预测术后复发风险的重要因素,而其他变量如癫痫持续时间也需要考虑。公认的神经病理学分类标准有助于识别术前预测因素,并有助于筛选可能从癫痫手术中获益的患者。

    Release date:2017-11-27 02:36 Export PDF Favorites Scan
  • 微小 RNA 和伴海马硬化的内侧颞叶癫痫:人类海马全微小 RNA 组谱

    内侧颞叶癫痫(mesial temporal lobe epilepsy, mTLE)是一种严重的以反复癫痫发作为特征的神经系统疾病。mTLE 通常伴有海马神经元变性导致的海马硬化(Hippocampal sclerosis,HS), 它是与 mTLE 患者耐药性相关的最常见的形态学改变。对 mTLE+HS 的认识不足使其治疗复杂化。mTLE+HS 的潜在病理机制可能涉及异常的基因表达调控,包括涉及微小 RNA(microRNA, miRNA)的转录后网络。 miRNA 表达调控在包括癫痫的多种疾病中都有报道。但是,mTLE+HS 的 miRNA 谱暂未被完全了解,需要进一步解决。在此,为了揭示 miRNA 的异常表达,我们关注了 33 例 mTLE+HS 患者和 9 具对照者尸检的海马 miRNA 分析。研究中,通过联合两种不同的 miRNA 分析方法,以及下一代测序技术和 miRNA 特异性实时定量聚合酶链式反应,我们显著降低了技术相关的偏移(最常见的是 miRNA 分析数据的假阳性)。这些方法结合起来明确并验证了 20 例癫痫患者海马中 miRNA 的表达改变。在 mTLE+HS 患者中,有 19 例 miRNA 上调,1 例下调。其中 9 种 miRNA 以往没有报道与癫痫有联系,19 例异常表达的 miRNA 可能调节与癫痫相关的靶点和通路(例如:钾离子通道,γ-氨基丁酸,神经营养因子信号传导和轴突导向)。研究通过明确 miRNA 在 mTLE+HS 中表达,扩展了当前对 mTLE+HS 中 miRNA 介导的基因表达调控的认知,包括 9 个新发现的 miRNA 异常表达及其可能的靶点。 这些发现进一步提升了基于 microRNA 的生物标志物或疗法的可能性。

    Release date:2018-03-20 04:09 Export PDF Favorites Scan
  • 良性内侧颞叶癫痫的研究进展

    颞叶癫痫(TLE)是指异常过度放电起源于一侧或双侧颞叶结构的癫痫,是最常见的成人局灶性癫痫,也是最常见的药物难治性癫痫。内侧(Mesial)TLE 是 TLE 的主要类型,手术切除致痫灶是有效治疗方法。然而,部分患者的症状则较轻,并且能够在服用或未服用抗癫痫药物治疗的情况下达到无限期的缓解期,被认为是良性(benign)MTLE,此类患者经常有发热发作和癫痫的家族史。目前研究者认为 MTLE 可能与海马硬化和遗传因素有关,文章就 bMTLE 的研究进展进行总结,以提高临床对其认识。

    Release date:2019-01-19 08:54 Export PDF Favorites Scan
  • 基于红藻氨酸和劳拉西泮联合给药的新型人类获得性颞叶癫痫动物模型

    红藻氨酸(Kainic acid,KA)是一种有效的谷氨酸类似物,用于诱导啮齿动物的神经退行性变和颞叶癫痫(TLE)。KA 可诱发严重的、持续的癫痫发作,即惊厥性癫痫持续状态(convulsive Status epilepticus,cSE),没有药物干预的情况下通常是致命的。在过去 30 年里,使用 KA 来建立人类癫痫动物模型毫无疑问被证明是有价值的,但显著的可变性和死亡率一直使结果变得不确定。这些问题很可能是 cSE 导致的,这是一种本质上可变且无法控制的全或无反应。然而,cSE 与人类疾病的相关性尚不确定,因为大多数癫痫患者从未经历过这种情况。该研究试图构建一种简单的、基于 KA 的 TLE 动物模型,以避免 cSE 及其混淆因素。成年雄性 Sprague-Dawley 大鼠分别接受皮下注射 KA(5 mg)和劳拉西泮(0.25 mg),剂量分别约为 15.0 mg/kg 和 0.75 mg/kg。持续的视频脑电图(VEEG)被用来监测急性癫痫的发作和检测自发性癫痫发作。免疫细胞化学、Fluoro-Jade B 染色和 Timm 染色被用来描述急性和慢性神经病理学改变。急性局灶海马癫痫发作在约 30 min 后开始并在几小时后自行终止。广泛的海马神经变性在 4 d 之后发现。在所有动物中自发性的局灶海马癫痫发作平均 12 d 之后开始。典型的海马硬化和苔藓纤维出芽的形成是长期神经病理学的特征。发病率和死亡率均为 0%。我们发现在联合注射低剂量苯二氮卓类药物时,KA 全身性给药的作用可局限于海马。这意味着劳拉西泮可以阻止痉挛性癫痫发作,而没有真正阻止癫痫电活动。这个创新的、无 cSE 的动物模型,可靠地模拟了获得性颞叶内侧癫痫所定义的特征:海马硬化和在长时间无癫痫发作后自发的海马起源的癫痫发作,并不伴显著的发病率、死亡率或无反应者。

    Release date:2019-03-21 11:04 Export PDF Favorites Scan
  • Surgical treatment for the temporal lobe epilepsy with hippocampal sclerosis: report of 42 cases

    ObjectiveTo explore the clinical features and surgical treatment effects of the temporal lobe epilepsy with hippocampal sclerosis.MethodsForty two patients diagnosed as temporal lobe epilepsy with hippocampal sclerosis and underwent protemporal lobectomy in Wuhan Brain Hospital from Jan. 2012 to Dec. 2018 were collected, which included 30 males and 12 females, with the age between 9 to 60 years. Their disease duration ranged from 3 to 10 years. The clinical manifestations showed complex partial seizure in 18 cases, partial-secondary –generalized seizure in 4 cases, and generalized tonic-clonic seizure in 20 cases. Based on their results of clinical manifestations, combined with MRI and VEEG results, all the patients underwent anterior temporal lobectomy (including the most parts of the hippocampus and amydala).ResultsThe postoperative pathology confirmed the diagnosis of hippocampal sclerosis. The follow-up of more than 1 year showed seizure-free in 38 cases, and significant improvement in 4 cases.ConclusionsTo the patients of temporal lobe epilepsy with hippocampal sclerosis, anterior temporal lobectomy should be performed (including the most parts of the hippocampus and amydala) if the VEEG monitoring results show that there are epileptic discharges in the ipsilateral temporal lobe. And the postoperative curative result is satisfactory.

    Release date:2019-05-21 08:51 Export PDF Favorites Scan
  • Altered spontaneous brain activity in mesial temporal lobe epilepsy with unilateral hippocampal sclerosis: a meta-analysis of resting-state functional magnetic resonance imaging

    Objective To identify the most consistent and replicable characteristics of altered spontaneous brain activity in mesial temporal lobe epilepsy patients with unilateral hippocampal sclerosis (MTLE-HS). Methods A systematic literature search was performed in PubMed, Embase, The Cochrane Library, China National Knowledge Infrastructure, Wanfang, and CQVIP databases, to identify eligible whole-brain resting state functional magnetic resonance imaging studies that had measured differences in amplitude of low-frequency fluctuations or fractional amplitude of low-frequency fluctuations between patients with MTLE-HS and healthy controls from January 2000 to January 2019. After literature screening and data extraction, Anisotropic Effect-Size Signed Differential Mapping software was used for voxel based pooled meta-analysis. Results Nine datasets from six studies were finally included, which contained 207 MTLE-HS patients and 239 healthy controls. The results demonstrated that, compared with the healthy controls, the MTLE-HS patients showed increased spontaneous brain activity in right hippocampus and parahippocampal gyrus, right superior temporal gyrus, left cingulate gyrus, right fusiform gyrus, and right inferior temporal gyrus; while decreased spontaneous brain activity in left superior frontal gyrus, right angular gyrus, right middle frontal gyrus, left inferior parietal lobule, left precuneus, and right cerebellum (P<0.005, cluster extent≥10). Conclusion The current meta-analysis demonstrates that patients with MTLE-HS show increased spontaneous brain activity in lateral and mesial temporal regions and decreased spontaneous brain activity in default mode network, which preliminarily clarifies the characteristics of altered spontaneous brain activity in patients with MTLE-HS.

    Release date:2019-11-25 04:42 Export PDF Favorites Scan
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